Caafimaadka, Cudurrada iyo Xaaladaha
Waa maxay cudurka Ollier. Ollier ee cudurka: ogaanshaha iyo daaweynta
Waxaad u malayn lahaa in lugaha ilmahaaga yar ama hub si tartiib ah u koraan? Waxaa laga yaabaa in cudurka Ollier uu. Waa cudur, taas oo ay jiraan aan caadi ahayn ee horumarinta laf ka mid ah lafaha, in uu yahay, oo ay Kobac la'aanta. Magacyada kale ee ku xusan cudurada - lafaha chondromatosis badan, gooni ah ama chondromatosis lafaha diskhondroplaziya. Uu cudurka ugu weyn ee horyaalka ahaa oo ku hadlaya magaca qalliinka Lyons Olier. Cudurku wuxuu helay iyo ku tilmaamay iyadoo la adeegsanayo X-rays ee 1899.
Waa maxay cudurka Ollier
Cudurka Tani waxa ay tilmaamaysaa aan caadi ahayn of lafaha lafaha, kaas oo iska leh cuduro badan, oo ay ku jiraan si fiican u yaqaan in ay dad badan oo kids hooyooyinka Kobac sinta.
Cudurku wuxuu sida caadiga ah teedu ee carruurnimada, sababta oo ah waxa markii hore u maleeyey in this cudurka carruurta. Waxaa hadda lagu cadeeyay in cudurada ka ayaa laga yaabaa inuu kulankiisii ugu horeysay ee dadka waaweyn (calaamadaha dhici kara xitaa kala duwan da'da 20-40 sano). Waa caadi ah lagu dhasho, laakiin waxay heleen in muddo ah ka dib - in carruurnimada hore ama in ay qaan - taas oo ah, waqtiga ee koritaanka degdeg ah, marka ay calaamadaha lahayo muuqata lafaha iyo / ama horumarinta aan caadi ahayn ee gacmaha iyo lugaha.
cudurka Ollier ee ku metaphyses of dheer lafaha embriyaha ee addimaha u muuqdaan in ay sameeyaan koritaan carjawda. Cudurka yeesho inta lafta, xajiga, iyo kala-goysyada oo ka mid ah gacmaha iyo cagaha, gaar ahaan cagaha iyo gacmaha, iyo sidoo kale in miskaha, laakiin waxaa la helay in ay feeraha, sternum iyo qalfoofka.
Koritaan ama enhondromy dhigi lakabka sare ee lafta khafiif ah iyo debcaan. Dhab ahaantii, waa buro-caanood in isku beddeli karaa malignant (tusaale ahaan, chondrosarcoma). Nasiib wanaag, tani dhacdo aad u dhif ah.
Inta lagu guda jiro koritaan qaangaadhnimada xasilinta iyo bedelay lafaha.
Sidaas darteed, cudurka Ollier - cudur la iska dhaxlo culus, kalshum lafaha cartilaginous kaas oo sidoo kale ay dhacdo iyo metaphyses adag (lafaha dhaadheer ee qoorta). Sababta ay dhacdo weli la ogeyn. Xaaladaha qaarkood, waa ah qof hidde xukuma autosomal.
Midka ah cudurada si diskhondroplaziey waa syndromes dhif maffucci iyo Proteus. Marka ugu horeysa, ka sameeyaan koritaan loo benign carjawda iyo cuuryaannimo lafaha, maqaarka hemangioma sameeyay marka laga reebo - baro casaan mugdiga ah qaabka aan caadi ahayn, oo ka kooban xididdada dhiigga. In labaad ee horumarinta burooyin aan halis ahayn in qaybo kala duwan oo jidhka ah.
Yaa u saameeyeen cudurka
Markii hore waxa la filayay, in lafaha chondromatosis dhif. Laakiin hadda, markii baaritaan X-ray ah waa la fuliyay ballaaran ku filan, waxa soo baxay in aanay failed. Haddii 20 sano ka hor, waxaa la tilmaamay 30 xaaladood in ay hadda yihiin labo jeer sida ugu badan.
Si loo go'aamiyo bilawga saxda ah sida caadiga ah wax aan macquul aheyn haddii dhalashada mid aan jirin waxbarasho joogto ah oo firfircoon oo isticmaalaya X-rays, gaar ahaan carruurnimada hore iyo horumarinta uurjiifka, marka, in fact, cudurka Ollier halkaas. Cudurku waa mid, iyadoo jidka ag fadhida, gabdhaha inta badan wiilasha shaaca ka qaaday ku dhawaad laba jeer.
calaamadaha
Ma aha inuu seego calaamadaha cudurka, waalidku waa inay ka digtoonaadaan, haddii ilmaha:
- raagayn horumarinta qaybaha qaar ka mid ah addimada / jirka,
- kaqabto calaamadeysan iyo yaraynta iyaga,
- lameness fiirsanayo;
- waxaa jira misalignment ee miskaha;
- dhaf-jooga ee meesha dharkiisa valgus ama nooca varus.
arrimood oo dhan waxay ka dhigi waxaa suurto gal ah in cudurka ilmahaaga Ollier.
Cudurku ma aha had iyo jeer isla markiiba cad at dhalashada, laakiin at da'da 1-4 sano, waxaad arki doontaa in ilmaha waa gaabis ah intii la filayay, sii kordhaya cagaha ama gacmaha. Tani waa calaamad ugu weyn ee cudurka, taas oo aan la iska indho tiri karin. Inta kale ee ilmuhu u kobcayo si caadi, inkastoo xaqiiqda ah in uu helay "cudurka Ollier ee."
Diskhondroplaziya inta badan saameeyaa mid addinka, si kastaba ha ahaatee waxaa jira kiisas of guuldaradii labada. Haddii cudurka uu taabtay hoos, ilmahaagu wuxuu noqon doonaa koritaanka hoose sabab u ah ay yaraynta. Gaar ahaan si xoog leh faaqidaad lafaha haddii habka bahal bilowday goor hore. Lahayo ku sii wado horumarka gancan gaabis ah. Dabcan, gaadhista cudurka, ayaa noqonaya gaaban, dhumuc weyn, beddelo wiiqmin, lameness ayaa lagu arkay. Waxaa laga yaabaa in a varus ama qaloocsan valgus ee jilibka ah (inta badan ka yar - dhamaadka proximal ee lafta bawdada ama foot), qalooca-dhabarta. atrophy muruqa in cudurkan ma joogo.
isbeddel weyn waxaa waajib ah in a phalanx, jab iyo, mararka qaarkood, metacarpals ah. Waxay soo gaabisay, kordhiyay, sirgaxan iyo carjawda ku jira enlightenments badan.
Cudurka tahay Ollier ee jab sabab u ah cudurka ay horumariyo lafta qaldan. Si kastaba ha ahaatee, jab inta badan muuqan baxda.
Comorbidities
Diskhondroplaziyu raaci karaan lesions ee xubnaha kale, inkastoo cudurada la xiriira horumarinta ma aha had iyo jeer. Gaar ahaan, in gabdhaha yar yar qaba cudurka Ollier ayaa laga yaabaa inuu dhaco teratoma of ugxan iyo hormoonada jidhka xanuunada, oo ay ku jiraan aad u daran, oo ay ku jirto caadada aad u hore iyo qaangaadhnimada fariida degdegsiimada lafoobid.
Si kastaba ha ahaatee, horumarka la soo laabtay si caadi ah iyadoo la fogeynayo buro ah ugxan.
Baadhista xanuunada
Si loo garto cudurka Ollier ee, marka hore loo baahan yahay in la sameeyo roentgen ah. Waxaa sidoo kale waa in biopsy laf iyo magnetic resonance imaging. Marka la ogaado cudurka, bukaanka u baahan baaritaan si joogto ah dhakhtar, haddii loo baahdo, si dhakhso ah loo ogaado isbedelka malignant in chondrosarcoma.
cudurka kala duwan
cudurka kala duwan ee cudurka Ollier ee, dhab ahaantii, ma lagama maarmaan ka dib markii X-ray, sababtoo ah sawirka waa chondromatosis aad u gaarka ah. Si kastaba ha ahaatee, kiis kasta waa shakhsi, laakiin set oo ah calaamadaha daran shiidaa soo noqnoqda, si dhakhaatiir waa in uu meesha ka saaro tiro ka mid ah cudurada la midka ah.
Roentgen tiraa atypical Chondrodystrophy, hemihypertrophy ama atrophy lafta, lahayo ku qabta riketis iyo qaar ka mid ah cudurada kale. Sidoo kale, ay sabab u tahay X-rays, waxaa laga reebaa cudurka Recklinghausen, oo sida caadiga ah waxaa lagu khaldaa cudurka Ollier. mabda'a ugu weyn - baahida loo qabo in la sameeyo x-ray lafaha oo dhan, halkii ay ka qayb ka mid ah.
Tilmaamaha daweynta
Diskhondroplaziya la joogo, nasiib daro, ma laha habab caqligal ah ee daaweynta. Taas bedelkeeda, tusaale ahaan, cudurada sida Kobac hip, chondromatosis loola dhaqmo oo keliya by saxo qalliinka ee lahayo ku. Xaaladaha qaarkood, waxa uu muujinayaa bedelka ah hip aan dabiici ahayn. Inta kale ee daaweynta bukaanka waa in ay helaan, - astaamaha iyo taageero.
qalliin waxaa inta badan lagu tilmaamay ee dadka waaweyn, tan iyo markii, sida uu sheegay indhaynta casri ah, markii la saxo qalliinka ee da'da dugsiga natiijada joogto ah ayaa la helay, taas oo macnaheedu yahay in dareenka daaweynta qalliin lagu sameeyey oo kaliya inta lagu guda jiro lahayo ku, laakiin ma aha firfircoon. Si kastaba ha ahaatee, in dhaawacyo daran qalliin suuragal ah in carruurta, gaar ahaan marka ay timaado faraha, kuwaas oo si weyn u margado ee cudurka Ollier.
Cudurku wuxuu u baahan dayactirka wadajirka iyo lafta: bukaanka muujiyay xidhashada kabaha oo lugaha, isticmaalka biraha lafaha iyo qalabka kale ee loo hagaajin goysyada. Bukaan-socodka waa in ay galaan si gaar ah loogu talagalay daawaynta cudurada iyo jimicsi adag ciyaaraha.
Waxtar leh sida jimicsi iyo layliyada on lagtiisa oo gaar ah. Waxay ka caawisaa si loo soo celiyo muruq iyo xoojinta ay seeduhu.
Odoroska
Sida laga soo xigtay cilmi, inta badan ee qaangaadhnimada, carjawda waxaa lagu bedelaa lafta (waxaa laga yaabaa in sababta xaaladaha dadka cudurka la ogaan aad u dhif ah). Si kastaba ha ahaatee, saadaasha ka yar tahay raduzhen in carruurta yaryar: lahayo ku, inkastoo si tartiib tartiib ah, laakiin waa horumar. Tani waa waxa uu yahay cudurka Ollier khatar ah.
Cudurku wuxuu teedu laftiisa si gaar ah ay dhacdo in kasta oo, in saadaasha guud ahaan adag tahay in la qiimeeyo unambiguously. Marka lesions badan waa cuntamin ka badan in ay dhacdo ah wax ka bedelidii goosgoos ah hal. Single lahayo ku keenaysaa in yaraynta ka mid ah mid ka mid ah addimada iyo halkan, by ay kaqabto, gaar ahaan marka ay timaado carruurta yaryar. Oo waa wax aan macquul aheyn si uu u xaliyo. Sidoo kale in horumarka hore ee kansar kordhiyaa halista ah ee cuuryaannimo kala duwan ee faraha.
Isbadal galay chondrosarcoma
In kasta oo xaqiiqda ah in isbadal malignant in view - chondrosarcoma - uusan inta badan dhacaan, weli waxaa jira fursad ah kansarka. Badanaa tani dhacdo in ay qaan, inkastoo tiro ka mid ah cilmi-baarista ee hadda muujinaysaa in ay dhici karaan wax badan ka dib. Sababtan awgeed, bukaanka waxa lagula talinayaa diskhondroplaziey wada tashi joogta ah dhakhtar iyo baaritaanka caafimaad.
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