Caafimaadka, Cudurrada iyo Xaaladaha
Somogyi Down syndrome ama chronic ah qiyaasta xad dhaafka insulin (SKHPI): calaamadaha, cudurka, daaweynta
Somogyi ee syndrome - cudur dhif ah laakiin hornimaadno, gaar ahaan dadka caanka ah qaba cudurka macaanka. Sida ay garan karaan oo haddii aad la daaweyn karaa?
syndrome Ra'yiga Somogyi
In diabetes u baahan xisaabinta sax ah qiyaasta insulinta, laakiin inta badan waxay noqon kartaa wax adag in la sameeyo, taas oo ben la dhibaatooyin. Natiijadan ayaa waxa uu noqonayaa badinta daroogada joogto Somogyi syndrome. In si kale loo dhigo, waa syndrome a chronic ah qiyaasta xad dhaafka insulin. saynisyahan American Michael Somogyi bartay this ifafaale ee 1959 iyo gabagabeeyey in qaadashada ah ee xaddi badan oo ah walaxda dhirfinaya hypoglycemia - hoos u dhac in heerarka sonkorta dhiigga. Tani waxay keenaysaa in kicinta ee hormoonnada iyo jawaab kontrinsulinovyh - celiska aheyd hyperglycemia (kordhay heerka sonkorta dhiigga).
Waxaa soo baxday in waqti kasta in heerka insulin, dhiiggu waa ka badan doonayo, in mid ka mid ah kiiska keentay in hypoglycemia, iyo wixii kale - si ay u cunid. sii daayo A hormoonnada keena isku bed kontrinsulinovyh joogtada ah ee heerka sonkorta dhiigga, taasoo keenta socodka ruxanaya of diabetes, iyo waxay keeni kartaa in ketonuria (acetone kaadida) iyo ketoacidosis (dhibaato of diabetes).
xaqiiqooyinka taariikheed
Insulin markii ugu horaysay si guul leh loo isticmaalay 1922, ka dib markii taas oo bilaabay baadhitaan dhamaystiran oo ah saamaynta ay jirka ku leeyihiin, tijaabo on xayawaanka iyo bini'aadanka qaadeen. Seynisyahanno ku ogaaday in qaadasho sare ee daroogada ee xoolaha keeni lama filaan ah hypoglycemic, inta badan waa in la dilaa. Waxaa la soo jeediyay in tiro badan oo ah waxyeello sun ah hoormoonka jirka. In kuwa sanadaha hore, daroogada loo isticmaalo in lagu daweeyo bukaanka qaba anorexia si ay u kordhiyaan miisaanka jirkooda. Tani waxay keentay in isbedel joogto ah caddadka gulukooska ee dhiiggaaga, kala duwanaansho ka hypoglycemia in hyperglycemia. Marka la dhameeyo of koorsada daawada bukaanka waxaad tustay calaamooyin of diabetes. Saameyn la mid ah ka dhacay maskaxda lagu daweeyo bukaannada qaba schizophrenia "naxdin leh insulin". Qaabka dhexeeya kordhay qiyaasta iyo in la kordhiyo insulin tusay glycemia iyo daaweynta sonkorowga. Tani waxay ifafaale uu noqday yaqaan mustaqbalka sida syndrome Somogyi.
calaamadaha
Sida a is-faham in jidhka la kulmin badinta chronic of insulin? Somogyi syndrome la muujiyey by calaamadaha:
- waxaa jira xumaatay guud ee caafimaadka, waxaa jira tabar ah,
- madax xanuun lama filaan ah, madax wareer, taas oo si weyn kadib markii qaadashada cuntada of carbohydrates tegi karo,
- hurdo u wareersan, uu murugeysan iyo maqaar saar, inta badan qarow,
- waxaa jira dareen joogta ah daal, hurdo,
- toos subaxdii adag, dadku dareemaan naxdin,
- muuqan kartaa aragti cawlan foomka of ceeryaamo hor inta uusan indhaha, xijaab ama biligleynaya baraha dhaldhalaalaya,
- isbeddelo ah niyadda, inta badan dhinaca xun,
- rabitaanka cuntada oo kordhay, miisaanka oo kordha.
calaamadaha noocan oo kale ah waxaa arrin welwel dawan, laakiin laga yaabaa in aanay noqon sabab cad for cudurka, sida ay yihiin calaamadaha cuduro badan oo. Sawir buuxa oo geedi socodka ka dhacda jidhka la ogan karo iyadoo la kaashanayo imtixaanada.
Baadhista xanuunada
Cilad-"Somogyi syndrome" caawin calaamadahan waa:
- muuqaalka jirkooda ketonka (acetone) kaadida,
- Tilmaamayaasha heer isbedbedelka glucose af badan oo degdeg ah ka yar yahay in sare oo dib u maalintii oo dhan,
- hypoglycemia toos ah ama awaamiir,
- glucose wanaajiyey ee hargabka,
- sonkorowga dara la sii kordhaya qiyaasood oo insulin iyo hagaajinaysaa la hoos u dhac.
cudurka syndrome Somogyi kiisaska intooda badan waa ay adag tahay, waayo, khubaro, daruuri ma aha tashi endocrinologist ah ku siin kara natiijada saxda ah isla markiiba. Tan waxa u sabab xaqiiqada ah in calaamadaha bukaanka iyo xanuunada ku dhaca jidhkiisa, waxay calaamad u karin sidii loo badin ah insulin, iyo hoos u dhaca. Sawirka daaweynta ee geedi socodka kuwanu waa isku mid, badinta chronic la ogaan karaa oo kaliya ka yar kormeer joogto ah iyo si taxaddar leh xirfad lafaguraa. Cilad ku salaysan tahay arrimo ay ka mid yihiin soo jeedinta caadiga ah clinical, gobolka hypoglycemic soo noqnoqda, a isbedbedelka sonkorta dhiigga oo sarreeya.
cudurka kala duwan
Somogyi in cudurka of syndrome waa si fudud wareersan la daliilka ugub ah "waaberiga", sida calaamadaha, kuwaas oo laba heley waa isku mid. Si kastaba ha ahaatee, waxaa jira farqi weyn. The ugub ah "waaberiga" waxaa laga helaa oo keliya ma aha in dadka qaba cudurka macaanka, laakiin sidoo kale in dadka caafimaadka qaba, wuxuu muujiyey hyperglycemia waaberiga. Tan waxa u sabab la'aanta ah ee heerarka insulin asalka ay sabab u tahay burburinta deg deg ah oo beerka ama sii daayo wanaajiyey hormone contrainsular subaxdii. Si ka duwan Somogyi syndrome, muujinta this ifafaale aan ka hormarey hypoglycemia. Si aad u gelin ogaanshaha sax ah waxaa lagama maarmaan ah in la ogaado heerka sonkorta dhiigga ka labo ilaa afar subaxdii, in bukaanka qaba chronic syndrome badinta waxaa la hoos u, iyo in bukaanka la waagu hyperglycemia uusan beddelo. Daaweynta cudurada yahay mid kasoo horjeeda: in kiiska ugu horreeya, qiyaas insulin waa la dhimay, ka dibna labaad - si loo kordhiyo.
Features of diabetes in syndrome ee Somogyi
isku dhafan ee macaan ay la syndrome ee xad dhaafka ah ee joogtada ah ee insulin (SKHPI) ku siinayaa saamayn dhaawici, cudurka si gaar ah u adag. Against asalka ah si joogto ah qaata qaadasho xad dhaaf ah hypoglycemia noqdo qaab qarsoon. Somogyi syndrome in diabetes ku muuqata in xaaladda guud ee bukaan-socodka, iyo dhaqankiisa.
isbedel kadis ah niyadda sabab la'aan - arrin joogto ah oo qaba cudurka sida. Marka hiwaayadaha cashar kasta oo ganacsi ama ciyaarta ka dib markii a halka ninka si lama filaan ah u lumiya xiisaha wax walba oo ka socda, waxa uu noqonayaa mid daalid iyo Cadami, jalaq u siin xaaladaha dibadda. Mararka qaar xanaaq sigan ama gardarada ku dhici karaa. Inta badan, waxaa jira rabitaanka cuntada oo kor u bukaan ah, laakiin, inkastoo taasi, mararka qaarkood waxaa jira fikrad xun in ay cunto, ninkii waa diiday inuu wax cuno. calaamadahan ka dhaca 35% bukaannada. cabashooyinka More caadiga ah waxaa ka mid ah weerarrada daciifnimo, wareer, madax xanuun, dhibaato hurdo. Qaar ka mid ah la soco ah iyo aragga oo lama filaan ah oo muddo kooban ah (foomka xijaab indhaha ka hor ama dhalaalaya "umado").
daaweynta
Daaweynta syndrome ay ku lug Somogyi xisaabinta sax ah qaadasho insulin. Ujeedada this, lacagta maamula waa in la beddelo, waxaa la dhimay by 10-20% hoos dhawrid adag ee bukaanka. Sidee dheer waxaa lagu daaweeyaa Somogyi syndrome? Iyadoo ku xiran tilmaamo shaqsi farsamooyinka la saxo kala duwan loo isticmaalo - dhakhso iyo mid gaabis ah. First sameeyay labadii toddobaad ee la soo dhaafay, kii labaadna wuxuu ahaa qaadataa 2-3 bilood.
Ugu jaleecada hore, mid ka mid ah u malaynayso in hoos u dhac ku dose insulin waxay keeni doontaa in ka lumay ee syndrome, laakiin ma aha. hoos u soconayn in xaddiga daroogada ay maamusho ma hagaajiyo koorsada of diabetes, daaweynta waa in ay adag. Wuxuu saameeyaa cunto (si caadi qadarka carbohydrates baabbi'iyey cunto), dhaqdhaqaaqa jirka. Insulin waxaa maamula cunto kasta ka hor. Kaliya in hab ballaaran dhali karaa natiijo wanaagsan in dagaalka ka dhanka ah syndrome ee Somogyi.
Odoroska
ogaanshaha waqtiyeysan ee syndrome chronic ah qiyaasta xad dhaafka insulin ayaa saadaal wanaagsan. Waa muhiim in la is ogow naftaada, ee signallo ee jirka, isbedel kasta oo xaaladda oo sii xumaaneysa ee caafimaadka isla markiiba la tasho dhakhtar, tusaale ahaan, ee Xarunta Endocrinology ee Waxbarashada (Moscow). Natiijada wanaagsan ee daaweynta doorka aasaasiga ah ka ciyaaray by xirfad iyo waayo-aragnimo ah ee dhakhtarka. Marka baarin syndrome saadaasha allifey: badinta socda ee insulin sii dari doontaa oo keliya xaalad ka mid ah bukaanka, waayo diabetes ka sii darayo.
ka hortagga
Meelaha ka hortagga SKHPI Main ka mid ah set oo ah tallaabooyin.
- In diabetes waa in si adag loo hogaansamey cunto si fiican isku aadiyo bukaanka iyo hubisaa in magdhow shiid carbohydrate. Qofka waa in la qorsheeyo cuntooyin aad, ay awoodaan si ay u xisaabiso qiimaha cuntada carbohydrate ah baabbi'iyey, soo saara bedelka ku filan oo sheyga, haddii loo baahdo.
- therapy Insulin waxaa la sameeyey bishii qaadasho loo baahan yahay bukaan gaar ah. hawsha dhakhtarka - haddii loo baahdo in la sameeyo la saxo, bukaanka - socdo dhacdooyinka ee u shaqeeyo.
- jimicsi joogto ah waa lagama maarmaan u ah bukaanada qaba cudurka macaanka, gaar ahaan haddii bukaanku waa yah ama shaqo fadhiyaan-hoos ah.
- la socodka joogtada ah ee cudurka, wada tashi ah endocrinologist jadwalka u gaar ah iyo sida loogu baahan yahay.
- qiimayn ku filan oo xaaladda jirka, caafimaadka, ogaanshaha deg deg ah ee calaamadaha laga shakiyo.
- Abuurista xaaladaha is-control ee nolol maalmeedka, daraasadda of bukaanada iyo xubnaha qoyska mabaadi'da is-xakamaynta.
Somogyi syndrome ee carruurta
Caruurta qaba cudurka macaanka, had iyo jeer ma socon kartaa isbedelada gobolka ee u shaqeeyo, inta badan taasi suurtogal ahayn, sidaas darteed, si loo xakameeyo koorsada cudurka - waalid daryeelaya. Si taxaddar leh u daawado ilmaha seexdo, sida ficilka insulinta waa inta badan ee habeenkii, iyo habdhaqanka ubadka badan oo sheegi kara. Marka muujinta syndrome ku seexan helo duulaan iyo maqaar saar, Ulasocto neefsashada buuq badan. ilmaha qaylinin ama qaylo hurdadii ay sabab u tahay qarow. Dadkuna culus, isla markiiba ka dib dhacdo wareer.
All daliilka kuwan - calaamad u tahay xaalad hypoglycemic. Maalinta oo dhan ilmaha weli gobolka flaccid, isagu waa cadho, xanaaq, uusan wax dan kulan ama waxbarasho. Arxandarro laga yaabaa in si lama filaan ah ay dhacaan, sabab la'aan, in koorsada ee kalfadhiga ah. dillaacay soo noqnoqda ee gardarada sigan, isbeddelo ah niyadda oo waa la saadaalin karin. Inta badan, caruurta la syndrome silco oo ka niyad-jabka. Daaweynta waxaa lagu fuliyaa on mabda'a isku mid ah sida in dadka waaweyn. Endocrinology Center ee Waxbarashada, tusaale ahaan, waxay ka caawisaa caruurta ula qabsadaan syndrome ee Somogyi.
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