Caafimaadka, Cudurrada iyo Xaaladaha
Ventriculomegaly uurjiifka - waa maxay?
Ventriculomegaly uurjiifka - waa cudurada a dhacda in nidaamka ventricular, sidaasna ay ku kordhiyaan xajmiga oo ka mid ah lateral intraventricular ee maskaxda, laakiin maskaxda uma siyaadiyo. In cudurkan xajmiga oo ka mid ah intraventricular lateral, halkii ay width laga yaabaa in ilaa iyo 15 mm.
Ventriculomegaly ilmaha caloosha ku waa sida iin gebi ahaanba go'doon, oo lagu dari karaa cillado kale ee la yaqaan. Waxa kale oo ay noqon kartaa qayb ka mid ah cillado koromosoomyada iyo curyaanimo badan.
Intii lagu guda jiray cilmi-baarista waxaa la ogaaday in haddii ay jirto ventriculomegaly cidlo ah ilmaha caloosha ku, ka dibna jaaniska ah cillado koromosoomyada waa weyn uga yar haddii ay dhacdo in lala isbedel kale. Sidoo kale, soo noqnoqoshada bandhigay koromosoomyada ku xiran tahay width oo ka mid ah intraventricular lateral, iyadoo ay hoos u dhacday jaaniska ah ogaanshaha noqdo sare.
In fulinta cilmiga sayniska ku adkeeyey in dhacdooyinka cudurkan ku saabsan yahay 0.6%. Ventriculomegaly uurjiifka waxaa inta badan laga helay at 17-34 toddobaad ee uurka. Sidoo kale, ku tiirsanaanta ee koromosoomyada ay sabab u tahay da'da qofka bukaanka ah, uur dhallinyaro ah, ayay la kulmay saddex jeer ka yar kuwa ka weyn 35 sano jir tahay.
Sidaas darteed, hadda waxaa lagu ogaaday in talagalay in lagu ogaado ventriculomegaly uurjiifka kuma filna kaliya in ay ultrasound ah, waxaa loo baahan yahay karyotyping uurjiifka.
In case of baaritaanka ultrasonograph qiimaha intraventricular lateral ee maskaxda, taas oo cudurka waxaa ka go'an, waa inuu noqdaa 10 mm. Marar badan, ventriculomegaly aan ogaado in marxaladaha hore ee uurka, iyo ogaanshaha waa suurto gal ku wareegsan dhamaadka 2 - hore bilood 3aad. Sida caadiga ah, muddada celcelis ahaan inta lagu jiro kaas oo ay macquul tahay in si sax ah uu sheego logu talagalay this waa gudahood 26 toddobaad ee uurka.
In qabashada ultrasound sax ventriculomegaly baaritaanada hooyada ku saabsan yahay 80%. natiijada been ah positive-waa ku saabsan 9% of sahan oo dhan.
Sida caadiga ah, dhakhtar fuliya baaritaanada hooyada, ay jiraan dhibaatooyin ku saadaalinta horumarka ilmaha, kuwaas oo lahaa xaaladda antepartum ventriculomegaly go'doon. Xaaladaha noocan oo kale ah waxaa loo dhexdhexaad ah ventriculomegaly go'doon. horumarka caadiga ah ee carruurta leh logu talagalay this wuxuu ku saabsan yahay 80%.
Dhimashada cudurkaan waa celcelis ahaan ku saabsan 14%. About 80% carruurta waxay leeyihiin horumarinta dheeraad ah oo caadi ah, iyo 8% lahaa leexashooyinkaasi dhexdhexaad ah oo ku saabsan 10% oo ka mid ah xaaladaha cudurrada guud ee dareemayaasha.
Ventriculomegaly ee dhallaanka ma ogola in ay si sax ah siin saadaasha wanaagsan ee horumarka dheeraad ah ee ilmaha. hillaadinta noocan oo kale ah waa in aad si taxadir leh u sameeyey, iyo dhaqanka oo ka mid ah waxbarashada iyo falanqaynta natiijada. dhasha Ventriculomegaly kuu ogolaanaya in aad siin saadaal wanaagsan oo kaliya haddii ay jirto ma jirto curyaanimo isu geeyey ee ilmaha, waxaa jira karyotype caadi ah, iyo dhaqdhaqaaqa uusan ka arkay kordhiyo width oo ka mid ah intraventricular lateral iyo width kama badna 15 mm. khubarada qaar ayaa rumaysan in ay tahay habka hal hab keeni kartaa cudurada ka sii daran dareemayaasha horumarka ilmaha.
Waxaa laga yaabaa in daaweyn ventriculomegaly anshaxa dhalmada dhaqanka jirka caafimaad. Waxaa la fuliyay laba marxaladood, marka hore ugu yaraan 20 cisho sameeyaa therapy jimicsi oo helay antihypoxants, iyo qeybtii labaad ee daaweynta waxaa lagu fuliyaa jimicsi therapy oo keliya, iyada oo diiradda la on load ku firfircoon oo ma guurto ah in muruqyada sagxada miskaha la lug. In joogitaanka ventriculomegaly uurjiifka, daaweynta bilaabi karaan marka size reer intraventricular lateral amarka of 12 mm.
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