Caafimaadka, Cudurrada iyo Xaaladaha
Rossolimo-Melkersson-Rosenthal syndrome: Calaamadaha, Daaweynta
Melkersson-Rosenthal syndrome Waxaa loo yaqaan cudur joogto ah, la triad calaamadaha muhiimka ah. cudurradana magaca waxaa jira laba magacyada dhakhaatiirta. Melkersson tilmaamay laba calaamadaha, iyo kii saddexaad ku calaamadeysan Rosenthal. Sidaas darteed, cudurka ayaa loo magacaabay ka dib markii labada dhakhaatiirta.
On Melkersson-Rosenthal syndrome
syndrome waa polyetiological. Of muhiimadda ugu weyn ee ay horumarka uu leeyahay dhowr arrimood:
- xasaasiyadda faafa;
- xanuunada vasomotor iyo cabista dhaxlo iyaga;
- cudurada of nidaamka durey degaanka ee madaxa iyo qoorta,
- Axdigu chronic cudurka odontogenic;
- hogaga.
In joogitaanka Melkersson-Rosenthal syndrome waa suurto gal neuro-side ay Bilowgii. Cudurku ku soo laabto waa xilliyeed. Inta badan ka syndrome Melkersson-Rosenthal saameeyaa dadka u dhexeeya 25 iyo 35 sano jir. cadhaysiinina karaa hypothermia ah cudurka iyo ku xadgudubka qamriga, iyo sidoo kale tiro ka mid ah daroogada. ku lug-geesoodka ah waa wax caadi ah - 75% ee kiisaska oo dhan. Aad ayay u yar - madaxyo simanna.
Calaamadaha Melkersson-Rosenthal syndrome
Syndrome muujiyey barar bushimaha iyo dhabannada. Markaas si tartiib ah u wiiqi muruqyada wejiga. Qofka ay adag tahay in la soo koobto indhaha, la hadal, gees oo afka ku shubtay dareere ah. In 30 boqolkiiba bukaannada horumarinta indhaha qalalan ama biyood. About 20% - wanaajiyey aragtida dhawaaqyo in sida xad in waxa uu noqonayaa mid xun. Maxaa kale ee sifaha calaamadaha syndrome Melkersson-Rosenthal? Ku dhowaad 80% ee bukaanada lagu daro barar bushimuhu wuxuu arkay casaada xoog leh, luuqada kordhay, oo ay dusha noqdo sinnayn, ku socoto. Half of bukaannada la kulma madax xanuun daran, qalal duub.
Maxaa kale oo lagu gartaa pathology ah?
Waa maxay calaamadaha of cerebral syndrome lagu gartaa Rossolimo-Melkersson-Rosenthal? Markii hore, waxaa lagama maarmaan ah in la xuso in Rossolimo - waa magaca dhakhtarka saddexaad, kuwaas oo in 1901 tilmaamay makroheylit ah (cudurka afka, kordhinta ay size) in isku darka paresis dareemaha wajiga. Later waxaa sameeyey Melkersson. Laakiin tan iyo cudurada description Rossolimo magiciisa mararka qaar loo isticmaalaa in cudurada ee horyaalka.
syndrome Cerebral shaaca ka qaaday by baaritaan Ujeedada. Waxaa lagu sheegi karaa sida:
- madax-xanuun (xanuunka dhanjafka);
- kaqabto wajiga ,
- curyaannimo wajiga of muruqyada wejiga ,
- calaamad lagophthalmos Bell;
- xerophthalmia;
- hyperacusis;
- dysarthria;
- bararka angioneurotic wajiga (sida caadiga ah dibnaha);
- carrabka fissured iyo macroglossia;
- dizgevzii iyo ageusia;
- cheilitis granulomatous.
Sida shaaca ka qaaday syndrome?
Melkersson-Rosenthal syndrome, taas oo uu leeyahay sawiro in this article la go'aamin karaa by cudurka. Xaaladdan oo kale, lagu qabtay:
- fuliyo;
- X-ray, haddii uu jiro tuhun ah in syndrome ayaa kacay ay sabab u tahay cudurada faafa (HIV, syphilis, cudur ku faraxnay, sarcoidosis);
- electromyography;
- imaging resonance magnetic of maskaxda;
- Baaritaanka Neuropathy.
Dabcan
Sidee waa cudur ka mid ah Melkersson-Rosenthal? syndrome wuxuu ku bilaabmaa bararka haragga. Waxaa markaas ayaa kobciya si xuubka afka. Waxa kordha cabirkooda dibinta: top - more hoose - yar. Waxaad la kulmi karaan xanuun ee dareemaha wajiga, ka dibna waxay yeeshaan curyaannimo.
Cudurku waxa lagu gartaa bilawga ba'an. Barar yeesho dhowr saacadood. Sida caadiga ah waa ballaaran ah oo si buuxda u bushimaha, kuwaas oo rinji cas oo dhalaalaya qabsatay, towns mararka qaar oo buluug u muuqataa. Qiyaastii afka sameysmi karaa dildilaaca. hadalka jeediya, dhibaatooyin la cunidda.
Sidee waa cudur joogto ah oo ah Melkersson-Rosenthal? syndrome ayaa sidoo kale ku bilaabmaa barar. Laakiin waxaa si joogto ah, waxay kordhisaa kaliya ama hoos at times. Barar ku kaydsan oo dhan wajiga iyo saabka afka.
Waa nooc ka mid dhif ah oo Melkersson-Rosenthal syndrome, marka dhabanada oo barara oo kaliya. Caadi ahaan, taasi waa uun mid ka mid ah. On the dhabannada dhinaca gudaha si cad imprinted ilkaha. Xaaladaas waxaa loo gudbiyaa by ereyga "Labada nin granulomatous." No calaamadaha caabuq.
daaweynta
Sidee Melkersson-Rosenthal syndrome? Dhakhaatiirta isticmaalaan hababka qalliinka ama muxaafid. Marka hore, bukaanka waxaa baaro si loo ogaado heley in uu keeni karo cudurka. daaweynta qalliinka ma looga hortago soo noq, oo waxaa loo isticmaalaa more ujeeddooyin isku qurxiyo, marka unugyada la gooya bushimihiisa.
Marka muxaafidka daaweynta natiijada ugu wanaagsan waxaa lagu gaari karaa isku-dar ah corticosteroids, antibiotics iyo daawooyin hantibaylihin. "Prednisolone" waxaa wada xilsaaray la "Oxytetracycline". Codso pyrogenic iyo wakiilada desensitizing. therapy MAR bakteeriyada. Haddii bukaanka waa xasaasi u ah stafylokok, ka dibna waxay khusaysaa "toxoid".
isagoo Bukaanka Melkersson-Rosenthal syndrome, ogaaday qoray qasabka ah, pantothenate calcium, nicotinic acid, vitamin A, loo qoondeeyey ah "komplamin" Waayo, hagaajinta wareegga dhiigga ee unugyada jilicsan. isticmaalka koorsada - 10 maalmood. A sidoo kale magacaabay "Cavintonum", "Tanakan" iyo "stugeron" in la qaado laga bilaabo 1 illaa 2 bilood. Bukaan-saaray sida "Nerobolum". Tani waa daroogada ah in ka hortagtaa gabowga. Ma loo magacaabay dejisa iyo daawada dajiyaha.
Daaweynta laga dhayayo
Waa maxay qaababka kale ee loo isticmaali karaa in ay ka gudbaan syndrome ee Melkersson-Rosenthal? Daaweynta noqon kartaa mariyo. Isla mar ahaantaana ka dhigay codsi ah oo cadar heparin. Waxay biiriyo Dimexidum, ka tago muddo 20 daqiiqo ah. Nidaamka waxaa fuliyay 3 ilaa 4 jeer maalin kasta. Koorsada - 3-4 todobaad.
Waayo, dibinta hoose waxaa loo isticmaalaa heparin elektrofarez. Nidaamka waxaa la sameeyaa maalin kasta. Marka loo isticmaalo hadda fizlechenii Bernard, laser helium-iyakana iyo ultrasound.
Codsiga of tuubooyinka iyo methyluracyl cadar waxaa loo isticmaalaa in geedi socodka bararka. qaris wajiga waxaa laga codsadaa muddo 20 daqiiqo ah, 2 ilaa 3 jeer maalin kasta. Intaa waxaa dheer, codsiyada waxaa laga sameeyey lacag keratoplasty.
Codso go'doominta (3-4 ml), diiran laba-boqolkiiba lidocaine, novocaine iyo trimecaine. Cirbadaha la sameeyey maalin ama laba maalmood oo kasta.
Cawaaqibta Melkersson-Rosenthal syndrome
Syndrome si deg deg ah uu noqdo chronic. Tan waxaa si xoog leh ka muuqataa muuqaalka qofka, taas oo ku margado iyo googooyey barar. Against asalka this inta badan niyad jabka iyo xanuunada maskaxda. Sababo la muddaada kordhay bushimaha iyo nin la calaaliyo dhib iyo liqidda, hadalka dhalanrog lagu arkay. The dildilaaca in muuqan marka barar iyo dhacaan kara bakteeriya waxyeelo ku keeni karo cudurada faafa. Tani waxay sidoo kale khuseysaa afka. Mararka qaar waxaa la daboolay dildilaaca. Intaa waxaa dheer, tani waxay halis kordhay sababo la xiriira dhaawac ilkaha xabka edematous, tusaale ahaan, inta lagu guda jiro Qaadka oo cunto ah.
Dadka ka cabanaya cudur this, waxaa lagu talinayaa in la cuno cunto adag, koorsooyinka marka hore, noocyo kala duwan oo badarka iyo waxyaabaha caanaha laga. Tani waa fududahay in la calaliyo cunto iyo yaraynaysaa suurtagalnimada of dhaawac xuubka afka. Miraha iyo khudaarta sidoo kale ay muhiim tahay, laakiin waxay u baahan yihiin in la jaro in xaleef yar oo ku dar in ay saladh. doodiisa waaweyn oo cunto ah wax fiican in la qaawi, in isticmaalka cuntada lagu cuno.
Similar articles
Trending Now