CaafimaadkaCudurrada iyo Xaaladaha

Akne Pemphigus: sababaha, calaamadaha, daaweynta, daawo. shalalka

Sidee cudur noocaas ah, sida pemphigus? Daaweynta iyo calaamadaha cudurkaan ayaa hoos looga hadlay. Waxa kale oo aad baran doontaa sababaha nidaamka cudurada iyo sida uu cudurka.

macluumaad aasaasi ah

Pemphigus, sawir kaas oo la soo bandhigay in this article, - koox ka mid ah, shalalka vesiculobullous dhif ah laakiin aad u daran, curyaamiyaa oo dili kara in saamayn maqaarka iyo xub-axaleedka.

Khubarada aqoonsado noocyada soo socda ee cudurka:

  • akne pemphigus;
  • foomka vegetans;
  • caleen,
  • seborroisk (waxaa laga yaabaa in magacyada sida Seniir-Usher syndrome, ama erythematous).

sifooyinka guud ee cudurka

akne Pemphigus ka dhigan category ka mid ah cudurrada maqaarka iyo unugyada subcutaneous, oo barwaaqaysan oo ah qaab raaga, la soo noqoshada soo noqnoqda.

Cudurkani waa hormone ku tiirsan. Waxaa lagu gartaa Dabcan horusocod ah, iyo sidoo kale formation of finan intraepidermal.

Inta badan, akne pemphigus saameeyaa dadka da'doodu tahay 50 sano ama ka badan.

Waa maxay sababta cudurkan dhaco? Sababaha horumarka cudurkan, waxaa jira mala kaliya.

Pemphigus: sababaha ay u badan tahay

Ka hor inta daaweynta, cudurka su'aashu waa mid aad u muhiim ah in aad ogaato sababta waa cudur, shalalka ka bukaan gaar ah kacay. Nasiib darro, helidda Jidka pemphigus waa ay adag tahay. Khubarada ayaa la dhibtoonayo dhaawac this muddo tobannaan sano badan. Inta lagu jiro wakhtigan waxay la Yimaadeen fikrad ah:

  • arrimaha Exogenous, ie qaadashada daawooyinka, oo ay ku jiraan penicillin iyo taagayo, iyo interferons kala duwan iyo waxyaabo kale.
  • arrimaha qoomiyadda, oo ay ku jiraan difaaca iyo hidaha.
  • arrimaha jirka (laga yaabaa in saamaynayaan helay gubasho ballaaran oo shucaac).
  • Hormoonada (failure tus hormoon in aadanuhu).
  • Fayrusyada (Herpesviruses).
  • Qaadashada cuntooyinka qaarkood.

Iyada oo ku saleysan arrimo kuwan, sharxaya dhacdo tahay cudurka, waxaannu ku tirinnaa: akne pemphigus noqon kartaa difaaca, hormoonada jidhka, faafa, neurogenic, sun ah, iwm Si kastaba ha ahaatee, waxaa la ogaadaa in ay jirto weli lama oga in isbedel kale waa aasaasiga ah ama ay xirtaan .. dabeecadda sare, iyadoo laga jawaabayo sababaha asalka.

Sidaas darteed, awood la'aanta in la ogaado sababta dhabta ah ee ka tixgeliyo cudurla si weyn u horjoogsadeen in ay cudurka ku habboon, si dad badan oo inta badan ay dhibaatooyin daran.

farsamo nucleation

Sidee waa horumarinta cudurada sida, sida pemphigus? stage hore Photo cudurka, waxaad ka arki kartaa in this article. Khubarada ayaa sheegaya in sababta keentay habka autoaggressive pathologic sida waa formation of antibodies borotiinka ka tirsan qoyska reer desmoglein. Arintaan wakiil nooc ka mid ah "xabagta" waxaa soo biiray unugyada epidermal ku xiga via xubno xira gaar ah, kuwaas oo loo yaqaan desmosomes.

limfosaytis Marka firfircoonaan iyo autoantibodies weeraraan desmogleins ah, unugyada epidermal laga soocaa midba midka kale, oo epidermis uu noqdo mid iska furan iyo "dhejiyo", oon si fudud u foojignaadaan off oo sakhiray in wax lays ee fangaska kala duwan oo bakteeriyada. In nidaamka bukaan eegida, this ifafaale waxaa lagu magacaabaa acantholysis.

Sida ka dhashay geedi socodka ku xusan bukaanku leeyahay finan maqaarka ah, iyo sidoo kale dhumucdiisuna. Isla mar ahaantaana waxay ka dhergaan exudate oo si joogto ah sii darayaan. Waqti ka, naqas waxaa diiray oo ka go'yaal, tiriska nudaha iyo sameynta malax iyo boogaha cudurka. Xaaladaha sare, formation sida xooga daboolaan dusha oo dhan ee jidhka.

macluumaadka taariikhiga ah

Asal ah khubarada cudurada maqaar oo aadan aqoon ku dhowaad waxba. Ereyga "pemphigus" codsatay in ay dhan lesions ee axal iyo maqaarka, acantholysis la socday, formation of goobooyin iyo askartii of go'yaal horumarinta boogo -sidii. Si kastaba ha ahaatee, in 1964 maqaal lagu daabacay wargeyska caafimaadka, oo waxgarasho ee dhakhaatiirta ku saabsan cudurka in su'aal, iyo sidoo kale waajahay iyo daaweynta bedelay. Tan iyo waqti in, jiritaanka unugyada ee plasma dhiiga ee bukaanka in desmogleina noqon Faraj ugu weyn ee aqoonsiga ee pemphigus.

By habka, 1971 uu daabacay maqaal kale ee dabiiciga ah, shalalka oo ka mid ah baaritaan faahfaahsan iyo hab ay of horumarinta cudurka this.

Calaamadaha ugu muhiimsan ee

Finan maqaarka ah, taasoo keentay in laga horumarinta bladderwort suuqnimo ama caadi ah, wakiil ugu horreysa ee calaamado cudur. Waa in la ogaadaa in noocan ah ee cudurka waxay badanaa ka dhacdaa. Sida laga soo xigtay khubaro, waxaa la xisaabay in 77% ka mid ah dhammaan foomamka la ogaado of pemphigus.

Dhaawacyada ee foomka of goobooyin saamayn ma aha oo kaliya maqaarka bukaanka, laakiin sidoo kale xabka ah ee afka iyo cunaha. Later ay Fidiyay on Addinka ah, xubnaha taranka dibadeed, wajiga iyo wixii la mid ah.

Waxa ay tahay inaad ogaato oo ku saabsan cudurrada maqaarka kuwanu? Sida caadiga ah, pemphigus si lama filaan ah uu yeesho. Sayidka on maqaarka caafimaad dusha sameeyey xiisado goobooyin yar in la faa'iido xawaaraha muuqaalka flaccid appreciable. waxyaabaha waa dareere nabarrada hufan (wax yar turbid).

Ka dib markii ay furan yihiin papules sameeyay dusha wiiqay, taas oo markii danbe la bogsiiyo, laakiin ka tago raad midabka ah brown.

Waayo, sida cudur, shalalka lagu gartaa socodka chronic daran ee foomka. Waa in la ogaadaa in shaqsiyaadka qaar ka mid ah iyada oo aan wax daaweyn ah ayaa lagu arkay horumar lama filaan ah, kaas oo lagu badalay xaalad xumeyd ee.

cudurada inta badan la socda akne pemphigus sare (candidiasis).

La'aan awgeed protein, dheecaanka iyo saamaynta faafa saadaal cudurkan la foomamka daran allifey.

Aqoonsiga cudurka

Sida shaaca ka qaaday akne pemphigus? Cilad cudurka waa la fuliyay isbitaalka. Joogitaanka cudurka la ogaado oo ku salaysan astaamaha caafimaad oo iyo natiijooyinka falanqayn.

hore waxaa ka mid ah:

  • calaamad A of asbestos-Hansen. Habkaani la ogaado adigoo riixaya farta ama galaas cover a (i.e., weli ma daalaeday) xumbo. Nidaamka noocan oo kale ah uu fududeeyaa askartii of epidermis ee aagga waa ku xiga si ay papules, iyo sidoo kale sii kordhaya meelaha ay sabab u tahay cadaadiska dareere gudahood unugga.
  • Calaamadaha Nikolsky. Habkaani la ogaado burburiyey entrainment xumbo la qabato oo ku xoqeen ayay qayb farta dusha maqaarka dhawrsan u dhow goobta dhaawaca. Haddaba waxaa jira askartii ka mid ah epidermis.

Waa in la ogaadaa in pemphigus suuqnimo calaamadahan ma aha gaar ah, iyo Baadhista. Waa in la xusuustaa in daliilka sida ku dhici kara cudurada kale.

sheybaar

Sidee lagu gartaa akne pemphigus? Daaweynta cudurka shalalka Waa in la fuliyo oo keliya ka dib markii baaritaan caafimaad. Si aad u ogaado sida cudur waxaa loo isticmaalaa:

  • Falanqaynta Histological, ku lug leh baaritaanka smears, ama faraha loogu yeero si ay u aqoonsadaan goobooyin unugyada acantholytic (ie, unugyada epidermal in soo maray isbedel morphological).

Waa in la ogaadaa in ku salaysan falanqaynta histological xogta in lagu gabagabeeyo in horumarka cudurka shalalka waa wax aan macquul aheyn. Tan waxa u sabab xaqiiqada ah in ay jiraan cudurada kale ee la sawir la mid ah.

  • Habka Immunofluorescence si loo ogaado kayd intracellular ee immunoglobulin G iyo A, sidoo kale si loo ogaado cudur waaweyn iyo kuwo yaryarba - desmoglein 3 iyo desmoglein-1. Habkani waa cudurka ugu badan oo sax ah.

Sidaas darteed, cudurka "pemphigus suuqnimo 'waxaa la dhigayaa salaysan xogta wadareed calaamadaha lagu daawayn iyo sawir caafimaad ee cudurka iyo natiijooyinka farsamo immunofluorescence iyo baaritaan histologic.

daaweynta

Bilowga horumarinta pemphigus akne bukaanka qoray glucocorticoids. Daroogooyinka in kooxdan helay qaadasho lama filaan ah. Magacaabista daroogada in tiro badan oo ah cadaymaha muhiimka ah. Iyadoo la tixgelinayo in ay sababo iyo waxyeelo, iyagu waa sare.

Maxaa dhacaya haddii cudur la is waydiinayo qori glucocorticoids? U diyaar garowga daaweynta puzyrchaki suuqnimo waxaa laga yaabaa in sida soo socota: "prednisolone" "Dexamethasone" iyo "Triamptsinolon".

Marka horumar bukaanka, i.e. ay ka maqan yihiin goobooyin cusub, qiyaasta daroogada waa la dhimay si tartiib tartiib ah oo u dhaqaaqin taageeraya si looga hortago soo noq. daaweynta noocan oo kale ah ee bukaanka dheer oo ku filan.

glucocorticoids sokow, bukaanka u xil laga yaabaa in wakiilada cytotoxic, immunosuppressants, oo ay ku jiraan "Daawada methotrexate", "azathioprine" ama "Prospidin". Waxay lagama maarmaan ah in meesha laga saaro dhibaatooyinka dhibaato ka dib markii uu qofku cuno ee daawooyinka aasaasiga ah waa.

Hababka kale daaweynta

Haddii ay jiraan calaamado muujinaya in in bukaanada cudurka shalalka in lagu daaweyn karo antibiyootiko, iyo daroogada oo taageera nidaamka wadnaha iyo, sharciyeynta cadaadiska dhiigga iyo kan caadiga ah hawlaha oo ka mid ah beerka iyo kelyaha.

Sidoo kale looga baahan yahay qaadashada of potassium-ka kooban wakiilada, calcium iyo fitamiino. Waayo, daawaynta jirka la mariyo ee daawooyinka anti-bararka pemphigus, infusions iyo decoctions of dhalatada oo loo isticmaali karaa.

Sidoo kale waa in la ogaadaa in, iyada oo ku xiran xaaladda bukaanka waxaa laga yaabaa in loo xilsaaray nidaamka sida gemabsorbtsiya, shubo dhiig iyo plasmapheresis.

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