Lennox-Gastaut syndrome (suuxdin)

Lennox-Gastaut syndrome - nooc ka mid ah kansarka beerka (myoclonic-astatic). cudurada jidhka noocan oo kale ah oo ku lug leh isku dhafan ee tonic iyo qalal atonic, qalal maqan atypical, dib u horumarinta maskaxda ee dhallaanka. Waayo, markii ugu horeysay ee cudurka muuqan kara in caruurta min hal ilaa shan, inta badan wiilasha.

Cudurku wuxuu sida caadiga ah uu yeesho iyadoo ay sabab u wareejiyay cudurada neerfayaasha carruurnimada, iyo bilaabmaa dhibic lama filaan ah in ilmaha. Muddo ka dib, waxaa jira qalal, suuxdin, muujiyaan horumarka maskaxda gaabis ah, iyo sirdoonka dhimay.

Tartiib tartiib, iyadoo koritaanka ilmaha, nooca qalal kala duwan. Dhici bedelay qayb ahaan, markii labaadna guud, weerar adag oo qalalka.

Sababta oo ah waxa lagu muujiyay Lennox-Gastaut syndrome

Si loo fahmo sababaha this syndrome waa adag ku filan, laakiin taariikhda yaqaan waa kuwa ugu muhiimsan.

• Yaraanshaha ayaa horumarka maskaxda.
• cudurada daran (meningitis, encephalitis, rubella).
• cudurada hidda bahal maskaxda (habdhiska, cudurada dheefshiidka, sclerosis tuberculous).
• ilmaha lagu dhaawacay marinka ee marinka dhalmada (qabatin dhalashada, dhalashada dhicis ah, iwm).
• dhaawac habdhiska dhimirka ee mudada dhalida, sidoo kale bixinta risk iyo qabatin.

calaamadaha PLGA

Lennox-Gastaut syndrome waxaa laga garan karaa calaamadaha ugu muhiimsan - waayo, suuxdin. Carruurta waxaa laga helaa "qalalka idiopathic", sidoo kale waxaa loola jeedaa noocyo kala duwan oo ah suuxdinta (calaamadaha) :

• paroxysms ah inuu dhaco,
• qalal atonic;
• maqnaanshaha atypical;
• qalal qayb ahaan;
• Qabqabashada sternocleidomastoid;
• qalal myoclonic-astatic;
• qalal tonic (caadi ahaan dhacaan inta lagu jiro hurdo weyn);
• TC guud qalal.

Bukaanka qaba syndrome ee Lennox-Gastaut sidoo kale gobolka sifo hurudda la kala guurka ah siman ee qallalka, dhimaal maskaxeed, garashada iyo cudura shakhsiyadda.

Soo ogaanshaha syndrome ee LH

Isla markii koowaad ee lagu garto cudurka waa in si deg deg ah u doonto kaalmo cilmiyeysan, wac ambalaas. Sida caadiga ah, cudurka cudurka waxaa lagu fuliyaa iyadoo la isticmaalayo ECG dhexeeya weeraro.

LH Syndrome Daaweynta

Lennox-Gastaut syndrome waxaa lagu daaweeyaa daawo iyo farsamooyinka qalliinka. Daawo ku qaadasho in ay dhali natiijo wanaagsan in wax ka badan 20% ee kiisaska. In habka daaweynta qalliin tirtirida dhibcood lama filaan ah, waa wax ku ool ah si ay u dhinto callosum gulkroppshormon ah (callosotomy). Sidoo kale, howlgal isticmaalka faray in kicinta ee dareemaha vagus iyo ka saarida burooyinka vascular iyo curyaanimo.

Si kastaba ha ahaatee, waxaa la ogaadaa in qalal caan this syndrome inta badan waa adag tahay in la daweeyo, Ugu dambaysta waxay keeni kartaa bukaanka inay cawaaqib bulshada iyo nafsi ah oo daran. qalal tonic shiidaa untreatable, taas oo keeni in ay hoos u sirdoonka.