Budd-Chiari syndrome

Budd-Chiari syndrome wuxuu dhacaa sabab u tahay soo rideynaa goosimo horusocod ah (xiritaanka ama cidhiidhi) Lumen ee xididka ah dheecaan ka galay beerka. Chiari rumeysan yahay in sababta ugu weyn - caabuq hoose oo ka mid ah xididdada cagaarshowga. Laakiin markii danbe waxaa la tilmaamay inay ku jiraan xaaladaha qaarkood, halka thrombosis of xididdada, cagaarshowga iyo cava vena liita.

suugaanta wuxuu sharaxayaa qiyaastii 200 xaaladood oo xaaqyna endoflebita in cagaarshowga xididdada (cudur , Budd-Chiari syndrome).

Iyadoo horumarinta koollo arantsieva thrombophlebitis, taas oo si toos ah faaruqdo xididka cagaarshowga bidix, xididka xudunta, iyo this syndrome laga yaabaa in la horumariyo in carruurnimada hore. qolof hoose oo ka mid ah xididdada cagaarshowga ama vena liita Vienna (ku dhow kulanka beerka) korayo, mararka qaarkood ku biiray by xinjiro dhiig. Waxaas oo dhan waxay keentaa xidhitaanka ama cidhiidhi ah Lumen ee xididka ah, kuwaas oo, ee jeedo, sababa horumarinta fadhiidka ah iyo riixo unugyada beerka.

Budd-Chiari syndrome ayaa sidoo kale waxa uu yeeshay ee heley kale: neoplasms malignant beerka, ee beeryarada, kelyaha, iwm, cudurada vascular dabeecadda guud. Cirrhosis sidoo kale gacan ka gaysan karaan in cidhiidhi oo ka mid ah xididdada cagaarshowga. Chiari syndrome keeni karaa deegaamaynta ah oo echinococcosis Gunma, actinomycosis, soo bax iyo wixii la mid ah.

Caafimaad ahaan, Budd-Chiari syndrome teedu calaamadaha cudurka ugu weyn, waxaa sababay bandhigay oo dheeraad ah ayaa sidoo kale ku xidhan tahay mudada qabsamin of xididada. Waxay u taagan tahay soo baxay af badan oo soo bixitaanka tartiib ah syndrome ah.

Xiisad qabsamin xididka cagaarshowga sababa muuqaalka lama filaan ah matag, xanuun Rubuca midigta sare ama epigastrium sabab u ah barar ku dhaca beerka, iyo sidoo kale hyperextension Glisson kaabsal, horumarisa ascites, waxaa jira jaalle ah oo yar yar.

hypertension Portal uu yeesho waqti isku mid ah sababta oo ah korodhka degdeg ah in cadaadiska ee sinusoids, cagaarshowga iyo xididdada.

Ascites qaba cudurka tani ma aha la daweyn karo oo la diuretics, dheecaan ayaa kor u si dhakhso ah mar kale ka dib markii paracentesis, mararka qaarkood u dabaal galo dhiiggeeda, waxa dhici karta in hydrothorax. Haddii biiray thrombosis in uu yeesho in cava ku vena liita, ka dibna waxaa barar ee jirka hoose, "madaxa Medusa", iyo cadaadiska fudud waxaa laga codsadaa in ay, dhiigga kor u kaco.

Iyadoo horumarinta ee wadarta qabsamin xididka cagaarshowga biiray thrombosis mesenteric, waxaa jira xanuun iyo shuban, dhibaatooyin maskaxda ah ka muuqan sababo la xiriira dhaawac gacanta beerka oo keeni dhimasho dhawr maalmood gudahood.

Mararka qaarkood syndrome ee Budd - Chiari, iyadoo xiritaanka qayb ka mid ah Lumen ee xididka laga yaabaa inuu dhaco sida cudur joogto ah oo wakhti dheer ah. Iyada oo nooca sida socodka waqtiga dhacdaa wareegga rahaamad: furaaya arooriye ah maqaarka maqaar saar, hypertension portal muuqataa, ka dibna ku biiray iyo xididdada qaradhku esophageal.

Waayo, cudurka joogaan lagama maarmaanka ah ee cadaadiska hoos xididdada beerka occlusal iyo kordhinta isku mar cadaadis portal ah, kaas oo la ogaado by hab ka mid ah hababka hepato- iyo splenomanometrii. Waxaa loo adeegsaday rentgenogepatografiya retrograde taas oo wakiilada ka duwan ayaa lagu bilaabaa xididka ah, cagaarshowga. Baadhista xanuunada Ultrasound ku salaysan tahay calaamadaha toos ah - sawirka xinjir dhiig ee xididka ah.

midabka aan cilmiga doplerrovskogo soo jeedin Budd-Chiari syndrome in:

• Joogitaanka isbedel waajihi beerka, caan ku daran beerka dufanka leh ama fibrosis unugyada beerka,

• Sawirka lahayn xididdada cagaarshowga, tacsida, tusaale ahaan, ay sabab u joogaan in ay Lumen celinayaan-positive in Lumen ah,

• cidhiidhi ah cava ku vena liita,

• calaamadaha hypertension portal, haddii cudurka waxaa sii dheeraaday.